DrugEvidence

Diseases / Idiopathic Pulmonary Fibrosis

Idiopathic Pulmonary Fibrosis

Disease

Idiopathic pulmonary fibrosis is a chronic progressive fibrosing interstitial lung disease of unknown cause characterized by worsening dyspnea, cough, and declining lung function. It primarily affects older adults and has a poor prognosis despite available antifibrotic therapies. Diagnosis typically requires multidisciplinary evaluation and exclusion of secondary causes.

Trials
565
Recruiting
73
Completed
306
With results
121

Last revised

Pipeline

Phase by status

PhaseRecruitingNot yetBy invitationActiveCompletedTerminatedWithdrawnSuspendedUnknownApproved for marketingNo longer availableTotal
Early Phase 1 2133 9
Phase 1 54268714 91
Phase 1/2 11911 13
Phase 2 20610651786 132
Phase 2/3 121 4
Phase 3 831124142 53
Phase 4 6222 12
Not applicable 95242515 78
Unknown 27931187352521 173

Trials started per year

2021
5
2022
41
2023
39
2024
34
2025
34
2026
45

Conditions studied, by phase

ConditionEarly Phase 1Phase 1Phase 1/2Phase 2Phase 2/3Phase 3Phase 4Not applicableUnknownTotal
Idiopathic Pulmonary Fibrosis 991131324531278173 565
Lung Diseases, Interstitial 131162821950 102
Pulmonary Fibrosis 110131313821 88
Lung Diseases 472435 25
Pulmonary Disease, Chronic Obstructive 1211713 25
Fibrosis 512511 24
Idiopathic Interstitial Pneumonias 21629 20
Cough 16231 13
Hypertension, Pulmonary 25222 13
Sarcoidosis 1210 13

Most active sponsors

#SponsorTrialsPhase 3
1Boehringer Ingelheim355
2Hoffmann-La Roche163
3Royal Brompton & Harefield NHS Foundation Trust111
4Bristol-Myers Squibb92
5Duke University73
6Genentech, Inc.74
7GlaxoSmithKline70
8Sunshine Lake Pharma Co., Ltd.71
9Actelion63
10Assistance Publique - Hôpitaux de Paris61

Most studied interventions

#InterventionTrials
1pirfenidone41
2nintedanib36
3Sildenafil Citrate8
4Blood Specimen Collection6
5BI 10155505
6Bosentan5
7pamrevlumab5
8treprostinil5
9Acetylcysteine4
10Exercise4

Evidence

Results reported
39.5%121 of 306 completed
Published
8.2%25 of 306 completed
Primary endpoint met
39.8%33 of 83 analyses
Median months to report
13

Documents disclosed

Protocol available
89
Statistical analysis plan
88
PubMed citations
68

Trial profile

Median enrollment
68
Median duration
29.1months
Countries
63
Study sites
5890

Who is enrolled

Adults
562
Children
40
Older adults
529
Healthy volunteers
101

Median enrollment by phase

Early Phase 1
20
Phase 1
26
Phase 1/2
23
Phase 2
74
Phase 2/3
139
Phase 3
325
Phase 4
54
Not applicable
40
Unknown
150

Where trials run

United States
233
United Kingdom
101
Germany
74
Italy
68
France
67
Australia
64
Canada
64
China
64
Spain
56
South Korea
50

Busiest cities

#CityCountryTrials
1LondonUnited Kingdom68
2PhiladelphiaUnited States64
3BirminghamUnited States63
4NashvilleUnited States60
5Los AngelesUnited States56
6New YorkUnited States54
7CharlestonUnited States50
8BostonUnited States48
9Salt Lake CityUnited States48
10Ann ArborUnited States47

Terminations

Terminated
49
Withdrawn
16
Suspended
1
Stopped for recruitment
1.8%10 of 565 trials

Stated reasons

Other / unclear
27
Recruitment
10
Business decision
8
Lack of efficacy
7
COVID-19
5
Safety
5
Funding
3
Regulatory
1

Reasons are grouped from the sponsor's own wording with a rule-based classifier; the original text is shown below.

Recently stopped

TrialStatusStated reasonStopped
NCT05785624 Terminated Terminated Sponsor decided to discontinue the study after review of clinical data by the iDMC. This decision was based on unblinded evaluation of clinical efficacy which showed a trend towards futility \& was not related to any safety concerns of vixarelimab. 2026-01-12
NCT04643769 Suspended Suspended Partnership activities ongoing 2025-12-30
NCT06317285 Terminated Terminated The study met futility criteria at pre-planned interim analysis, showing no clinical efficacy of the investigational drug. Based on the lack of efficacy at the interim data review, the sponsor decided to terminate the study. 2025-10-01
NCT06360094 Terminated Terminated Sponsor decision 2025-09-02
NCT05349760 Withdrawn Withdrawn to focus resources on other studies 2025-06-30
NCT06097260 Terminated Terminated DSMB recommendation 2025-04-04
NCT05359965 Terminated Terminated Lack of enrollment 2025-02-11
NCT05032066 Terminated Terminated The trial was terminated due to not meeting primary or key secondary endpoints. 2025-01-02
NCT04263727 Terminated Terminated Sponsor decision to terminate study 2024-11-21
NCT05497284 Terminated Terminated Sponsor Decision 2024-09-26

Trial records